Abstract
INTRODUCTION Budd-Chiari syndrome is a rare disease defined by obstruction of the hepatic portal vein. Its association with celiac disease is rare. CASE We report the case of a 28-year-old woman who presented with celiac disease associated with Budd-Chiari syndrome for which no cause could be found. A gluten-free diet and antivitamin K treatment led to a favorable outcome. DISCUSSION This case and a review of the literature suggest that the pathogenesis of these two disorders is linked.